Desmoplastic fibroma: A rare entity
نویسندگان
چکیده
Desmoplastic fibroma (DF) is an extremely rare benign intraosseus, locally aggressive bone tumor with an incidence of 0.11% of all primary bone tumors. The most common sites of involvement are the mandible and the metaphysis of long bones. Histologically and biologically, desmoplastic fibroma mimics extra-abdominal desmoid tumor of soft tissue. A 25-year male presented to outpatient department with increasing pain in left hip region since 2 months. Imaging investigations revealed a multiloculated cystic lesion in left femoral region. Curettage material was sent to our department. On histopathology, sections examined showed spindle-shaped cells without cytological atypia and abundant collagen production confirming the diagnosis of desmoplastic fibroma.
منابع مشابه
Multifocal desmoplastic fibromas of the mandible.
Desmoplastic fibroma is a locally aggressive benign fibrous tumor of bone that has been reported in both the maxillofacial skeleton and the long bones. Desmoplastic fibroma of the extremities was first reported by Jaffe1 in 1958. The first description of this entity involving the jaws was reported by Griffith and Irby2 in 1965. In rare instances, multifocal desmoplastic fibromas have been repor...
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